Page 146 - journal-6-3-Full
P. 146
Journal of Thai Traditional & Alternative Medicine Vol. 6 No. 3 September-December 2008 Ûıı
°“√‡ª≈’ˬπ·ª≈ß∑’Ë»Ÿπ¬å°≈â“¡‡π◊ÈÕ„π ¡Õß à«π‡¡¥—≈≈“ - „∫Àπâ“°≈ÿà¡Õ“°“√‡Õ§‚∑√·¥§∑’¬å≈’¬å¥‘¬å ‡æ≈‡ ’¬ - ‡§≈äø∑‘ß
ÕÕ∫≈Õß°“µ“ ·≈–¡’°“√‡ ◊ËÕ¡ ≈“¬πŸ‡§≈’¬ ¢Õ߇´≈≈å (ectrodactyly-ectodermal dysplasia-clefting) Àπ⓺“°
ª√– “∑∑’Ëæ◊ÈπÀâÕß ¡Õß ÀâÕß∑’Ë Ù ‚Àπ° §“ß„À≠à ª“°Àπ“ ª“°·À«à߇楓π‚À«à øíπ®”π«π
πâÕ¬´’ˇ≈Á° ®¡Ÿ°≈—°…≥–Õ“π¡â“ º¡·≈–¢π§‘È«∫“ß¡“° ’ÕàÕπ
- „∫Àπâ“°≈ÿà¡Õ“°“√ ¥Ÿ‡æ√ (Dupre syndrome) §Õ·¢Á߇ªìπ ‰¡à¡’¢πµ“ ; ‚√§°√√¡æ—π∏ÿå∂à“¬∑Õ¥·∫∫¬’π‡¥àπ
Õ“°“√· ¥ß¢Õß°“√√–§“¬‡§◊Õß∑’ˇ¬◊ËÕÀÿâ¡ ¡Õß √à«¡°—∫¡’‰¢â
À√◊Õ¿“«–¢“¥πÈ” ; ‚√§‡¬◊ËÕÀÿâ¡ ¡ÕßÕ—°‡ ∫ - „∫Àπâ“°≈ÿà¡Õ“°“√‡Õ¥‚¥«’ å (Eddowes syndrome) µ“¢“«
’øÑ“ ; æ∫„π‚√§°√–¥Ÿ°‡ª√“–°√√¡æ—π∏ÿå
- „∫Àπâ“°≈ÿà¡Õ“°“√ ¥—∑™å- ‡•π∑—§•’¬å (Dutch-Kentucky
syndrome) Õ⓪“°‰¥â‰¡à‡µÁ¡∑’Ë (¡’ªí≠À“°“√„ÀâÕ“À“√∑“√°); - „∫Àπâ“°≈ÿà¡Õ“°“√‡Õ¥«“√å¥ å (Edwards syndrome) À—«‡ªìπ
‚√§°√√¡æ—π∏ÿå∂à“¬∑Õ¥·∫∫¬’π‡¥à𠇪ìπµ—Èß·µà§≈Õ¥ §¡¡. —π√Ÿª∑âÕ߇√◊Õ§«Ë” À√◊Õ«‘√Ÿª·∫∫Õ◊Ëπ ¢“°√√‰°√≈à“߇≈Á° Àπ—ß
°≈ÿà¡Õ“°“√ ∑√‘ ¡— ªá ‘«-‚¥·§¡æå‚∑·¥§∑’¬å≈’¬å µ“µ° ÀŸµË” °√–®°µ“¢ÿàπ §Õªï° ; ‚√§°√√¡æ—π∏ÿå¡’‚¶√‚¡‚ ¡
Ò¯ ‡°‘π §¡¡. °≈ÿà¡Õ“°“√‰∑√‚ ¡’¬å Ò¯
- „∫Àπâ“°≈ÿà¡Õ“°“√ ¥—¬•å-·¥ø«‘¥Õøøá (Dyke-Davidoff
syndrome) ´’°ÀπⓉ¡à ¡¡“µ√ Õ—¡æƒ°…åÀ√◊ÕÕ—¡æ“µ ; - „∫Àπâ“°≈ÿà¡Õ“°“√π“߉¡â ; ¥Ÿ Williams syndrome
¿“«– ¡Õß´’°Àπ÷Ë߉¥â√—∫∫“¥‡®Á∫À√◊Õ‡ªìπ‚√§√⓬
- „∫Àπâ“°≈ÿà¡Õ“°“√‡Õ≈ “Œ’¬å-«Õ‡∑Õ√å å (Elsahy-Waters
- „∫Àπâ“°≈ÿà¡Õ“°“√¥—¬•å-·¥ø«‘¥Õøøá-·¡ —π (Dyke- syndrome) À—« —Èπ à«π°≈“ß„∫Àπâ“¥âÕ¬‡®√‘≠ µ“Àà“ß
Davidoff-Masson syndrome) °–‚À≈°»’√…–·≈–‰ π— µ“‡À≈à Àπ—ßµ“µ° ¥—Èß·≈–ª≈“¬®¡Ÿ°°«â“ß ‡æ¥“𪓰‚À«à
‡®√‘≠‡µ‘∫‚µ‡°‘π; ‚√§ ¡ÕßΩÉÕ≈’∫¢â“ßÀπ÷Ë߉¡à∑√“∫ “‡Àµÿ øíπ«‘√Ÿª; ‚√§°√√¡æ—π∏ÿå∂à“¬∑Õ¥·∫∫¬’π¥âÕ¬ À√◊Õ·∫∫
æ∫µ—Èß·µà§≈Õ¥ ‚¶√‚¡‚ ¡‡æ»‡ÕÁ°´å §¡¡. branchio-skeleto-genetal syn-
drome
- „∫Àπâ“°≈ÿà¡Õ“°“√π—¬π嵓 øíπ π‘È« ‡®√‘≠º‘¥ª√°µ‘ (dyspla-
sia oculodentodigitalis syndrome) ≈Ÿ°µ“‡≈Á° ®¡Ÿ°‡≈Á° - „∫Àπâ“°≈ÿà¡Õ“°“√‰Ωª“πº‘«Àπ—ß (epidermal naevus syn-
·≈–√Ÿ‡ªî¥Àß“¬ º‘«øíπ¡’√‘È«√Õ¬º‘¥ª√°µ‘ ; ‚√§°√√¡æ—π∏ÿå drome); ¥Ÿ∑’Ë °≈ÿà¡Õ“°“√µâÕ°√–®°√à«¡ ‘«‡ ’Ȭπ·µà°”‡π‘¥
∂à“¬∑Õ¥·∫∫¬’π‡¥àπ §¡¡. °≈ÿà¡Õ“°“√ ‡¡‡¬Õ√å- 噫‘§‡§Õ·√∏
·≈–‡«¬å‡ÕÕ√å - „∫Àπâ“°≈ÿà¡Õ“°“√‰ â‡≈◊ËÕπ –¥◊Õ ≈‘Èπ‚µ √à“߬—°…å
(exomphalos-macroglossia-gigantism syndrome) ; ¥Ÿ
- „∫Àπâ“°≈ÿà¡Õ“°“√‡Õ´’∑’‡Õ™πÕ°·À≈àß (ectopic ACTH syn- ∑’Ë °≈ÿà¡Õ“°“√ ‡∫§§å«‘∏-«’‡¥Õ¡“ππå
drome) ≈—°…≥–‡À¡◊Õπ‚√§§ÿ¨‘ß ; ‚√§‡π◊ÈÕßÕ° √â“߇մ’∑’
‡Õ™πÕ°µàÕ¡‰√â∑àÕ ‡™àπ ¡–‡√Áߪե‡´≈≈åµ—«‡≈Á°, ·Õ¥’‚π¡“ - „∫Àπâ“°≈ÿà¡Õ“°“√‡¥Á°·Õ≈°ÕŒÕ≈å (fetal alcohol syn-
À≈Õ¥≈¡ drome) ¢“°√√‰°√∫π‡≈Á°¡“°, Àπ⓺“°‚Àπ°, §“߬◊Ëπ, ™àÕß
Àπ—ßµ“ —Èπ, ≈Ÿ°µ“‡≈Á°, °√–®°µ“¢ÿàπ, —π¢â“ß®¡Ÿ°°«â“ߪî¥
- „∫Àπâ“°≈ÿà¡Õ“°“√º≈‘µŒÕ√å‚¡ππÕ°·À≈àß (ectopic hor- ¡ÿ¡™àÕßµ“ æ∫µ—Èß·µà·√°§≈¥®“°¡“√¥“¢’ȇÀ≈â“.
mone syndrome) ≈—°…≥–‡À¡◊Õπ‚√§§ÿ¨‘ß §¡¡. °≈ÿà¡
Õ“°“√æ“√“‡Õπ‚¥‰§√πå - „∫ÀπⓉ¡∑√—≈ (mitral facies, mitrotricuspid facies) ·°â¡
’·¥ß°ÿÀ≈“∫ ·≈–‡ÀÁπÀ≈Õ¥‡≈◊Õ¥ΩÉÕ¬‚ªÉßæÕß®”π«π¡“°