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Journal of Thai Traditional & Alternative Medicine                   Vol. 6 No. 3 September-December 2008 Ûıı



              °“√‡ª≈’ˬπ·ª≈ß∑’Ë»Ÿπ¬å°≈â“¡‡π◊ÈÕ„π ¡Õß à«π‡¡¥—≈≈“  - „∫Àπâ“°≈ÿà¡Õ“°“√‡Õ§‚∑√·¥§∑’¬å≈’¬å¥‘¬å ‡æ≈‡ ’¬ - ‡§≈äø∑‘ß

              ÕÕ∫≈Õß°“µ“ ·≈–¡’°“√‡ ◊ËÕ¡ ≈“¬πŸ‡§≈’¬ ¢Õ߇´≈≈å       (ectrodactyly-ectodermal dysplasia-clefting) Àπ⓺“°
              ª√– “∑∑’Ëæ◊ÈπÀâÕß ¡Õß ÀâÕß∑’Ë Ù                     ‚Àπ° §“ß„À≠à ª“°Àπ“ ª“°·À«à߇楓π‚À«à øíπ®”π«π
                                                                  πâÕ¬´’ˇ≈Á° ®¡Ÿ°≈—°…≥–Õ“π¡â“ º¡·≈–¢π§‘È«∫“ß¡“°  ’ÕàÕπ

             - „∫Àπâ“°≈ÿà¡Õ“°“√ ¥Ÿ‡æ√ (Dupre syndrome) §Õ·¢Á߇ªìπ  ‰¡à¡’¢πµ“ ; ‚√§°√√¡æ—π∏ÿå∂à“¬∑Õ¥·∫∫¬’π‡¥àπ
              Õ“°“√· ¥ß¢Õß°“√√–§“¬‡§◊Õß∑’ˇ¬◊ËÕÀÿâ¡ ¡Õß √à«¡°—∫¡’‰¢â
              À√◊Õ¿“«–¢“¥πÈ” ; ‚√§‡¬◊ËÕÀÿâ¡ ¡ÕßÕ—°‡ ∫           - „∫Àπâ“°≈ÿà¡Õ“°“√‡Õ¥‚¥«’ å (Eddowes syndrome) µ“¢“«

                                                                   ’øÑ“ ; æ∫„π‚√§°√–¥Ÿ°‡ª√“–°√√¡æ—π∏ÿå
             - „∫Àπâ“°≈ÿà¡Õ“°“√ ¥—∑™å- ‡•π∑—§•’¬å (Dutch-Kentucky

              syndrome) Õ⓪“°‰¥â‰¡à‡µÁ¡∑’Ë (¡’ªí≠À“°“√„ÀâÕ“À“√∑“√°);  - „∫Àπâ“°≈ÿà¡Õ“°“√‡Õ¥«“√奠å (Edwards syndrome) À—«‡ªìπ
              ‚√§°√√¡æ—π∏ÿå∂à“¬∑Õ¥·∫∫¬’π‡¥à𠇪ìπµ—Èß·µà§≈Õ¥ §¡¡.   —π√Ÿª∑âÕ߇√◊Õ§«Ë” À√◊Õ«‘√Ÿª·∫∫Õ◊Ëπ ¢“°√√‰°√≈à“߇≈Á° Àπ—ß
              °≈ÿà¡Õ“°“√ ∑√‘ ¡—  ªá ‘«-‚¥·§¡æå‚∑·¥§∑’¬å≈’¬å       µ“µ° ÀŸµË” °√–®°µ“¢ÿàπ §Õªï° ; ‚√§°√√¡æ—π∏ÿå¡’‚¶√‚¡‚ ¡

                                                                  Ò¯ ‡°‘π §¡¡. °≈ÿà¡Õ“°“√‰∑√‚ ¡’¬å Ò¯
             - „∫Àπâ“°≈ÿà¡Õ“°“√ ¥—¬•å-·¥ø«‘¥Õøøá (Dyke-Davidoff

              syndrome) ´’°ÀπⓉ¡à ¡¡“µ√ Õ—¡æƒ°…åÀ√◊ÕÕ—¡æ“µ ;   - „∫Àπâ“°≈ÿà¡Õ“°“√π“߉¡â ; ¥Ÿ Williams syndrome
              ¿“«– ¡Õß´’°Àπ÷Ë߉¥â√—∫∫“¥‡®Á∫À√◊Õ‡ªìπ‚√§√⓬
                                                                - „∫Àπâ“°≈ÿà¡Õ“°“√‡Õ≈ “Œ’¬å-«Õ‡∑Õ√å å (Elsahy-Waters

             - „∫Àπâ“°≈ÿà¡Õ“°“√¥—¬•å-·¥ø«‘¥Õøøá-·¡  —π (Dyke-     syndrome) À—« —Èπ  à«π°≈“ß„∫Àπâ“¥âÕ¬‡®√‘≠ µ“Àà“ß
              Davidoff-Masson syndrome) °–‚À≈°»’√…–·≈–‰ π—        µ“‡À≈à Àπ—ßµ“µ° ¥—Èß·≈–ª≈“¬®¡Ÿ°°«â“ß ‡æ¥“𪓰‚À«à
              ‡®√‘≠‡µ‘∫‚µ‡°‘π; ‚√§ ¡ÕßΩÉÕ≈’∫¢â“ßÀπ÷Ë߉¡à∑√“∫ “‡Àµÿ  øíπ«‘√Ÿª; ‚√§°√√¡æ—π∏ÿå∂à“¬∑Õ¥·∫∫¬’π¥âÕ¬ À√◊Õ·∫∫

              æ∫µ—Èß·µà§≈Õ¥                                       ‚¶√‚¡‚ ¡‡æ»‡ÕÁ°´å §¡¡. branchio-skeleto-genetal syn-
                                                                  drome
             - „∫Àπâ“°≈ÿà¡Õ“°“√π—¬π嵓 øíπ π‘È« ‡®√‘≠º‘¥ª√°µ‘ (dyspla-

              sia oculodentodigitalis syndrome) ≈Ÿ°µ“‡≈Á° ®¡Ÿ°‡≈Á°  - „∫Àπâ“°≈ÿà¡Õ“°“√‰Ωª“πº‘«Àπ—ß (epidermal naevus syn-
              ·≈–√Ÿ‡ªî¥Àß“¬ º‘«øíπ¡’√‘È«√Õ¬º‘¥ª√°µ‘ ; ‚√§°√√¡æ—π∏ÿå  drome); ¥Ÿ∑’Ë °≈ÿà¡Õ“°“√µâÕ°√–®°√à«¡ ‘«‡ ’Ȭπ·µà°”‡π‘¥

              ∂à“¬∑Õ¥·∫∫¬’π‡¥àπ §¡¡. °≈ÿà¡Õ“°“√ ‡¡‡¬Õ√å- å™«‘§‡§Õ·√∏
              ·≈–‡«¬å‡ÕÕ√å                                      - „∫Àπâ“°≈ÿà¡Õ“°“√‰ â‡≈◊ËÕπ –¥◊Õ ≈‘Èπ‚µ √à“߬—°…å
                                                                  (exomphalos-macroglossia-gigantism syndrome) ; ¥Ÿ

             - „∫Àπâ“°≈ÿà¡Õ“°“√‡Õ´’∑’‡Õ™πÕ°·À≈àß (ectopic ACTH syn-  ∑’Ë °≈ÿà¡Õ“°“√ ‡∫§§å«‘∏-«’‡¥Õ¡“ππå
              drome) ≈—°…≥–‡À¡◊Õπ‚√§§ÿ¨‘ß ; ‚√§‡π◊ÈÕßÕ° √â“߇մ’∑’

              ‡Õ™πÕ°µàÕ¡‰√â∑àÕ ‡™àπ ¡–‡√Áߪե‡´≈≈åµ—«‡≈Á°, ·Õ¥’‚π¡“  - „∫Àπâ“°≈ÿà¡Õ“°“√‡¥Á°·Õ≈°ÕŒÕ≈å (fetal alcohol syn-
              À≈Õ¥≈¡                                              drome) ¢“°√√‰°√∫π‡≈Á°¡“°, Àπ⓺“°‚Àπ°, §“߬◊Ëπ, ™àÕß
                                                                  Àπ—ßµ“ —Èπ, ≈Ÿ°µ“‡≈Á°, °√–®°µ“¢ÿàπ,  —π¢â“ß®¡Ÿ°°«â“ߪî¥

             - „∫Àπâ“°≈ÿà¡Õ“°“√º≈‘µŒÕ√å‚¡ππÕ°·À≈àß (ectopic hor-  ¡ÿ¡™àÕßµ“ æ∫µ—Èß·µà·√°§≈¥®“°¡“√¥“¢’ȇÀ≈â“.
              mone syndrome) ≈—°…≥–‡À¡◊Õπ‚√§§ÿ¨‘ß §¡¡. °≈ÿà¡
              Õ“°“√æ“√“‡Õπ‚¥‰§√πå                               - „∫ÀπⓉ¡∑√—≈ (mitral facies, mitrotricuspid facies) ·°â¡

                                                                   ’·¥ß°ÿÀ≈“∫ ·≈–‡ÀÁπÀ≈Õ¥‡≈◊Õ¥ΩÉÕ¬‚ªÉßæÕß®”π«π¡“°
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